Tuần hoàn Fontan sau nửa thế kỷ

Le Minh Khoi, Nguyen Hoang Dinh, Truong Quang Binh

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Abstract

Functional single ventricle was described at the end of the 17th century. This is a special group of congenital heart disease characterized by the high complexity and diversity of anatomic lesions as well as changes in hemodynamics and cardiovascular physiology. Fontan procedure was succesfully carried out for the first time in 1968, half a century ago, which could be considered as a revolutionary leap in the field of cardiovascular surgery. The Fontan procedure, in parallel with innovation and refinement in surgical techniques, interventional cardiology, medical management as well as breakthrough scientific knowledge in Fontan circulation, has signigficantly improved the outcomes of patients suffering from functional single ventricle increasing lifespan, reducing complications, enhancing quality of life. Fontan patients are, however, still seen as a group of patients with compensated heart failure and constantly are at risk of decompensation at any time. Complications associated with Fontan circulation always put clinicians at tremendous challenges. This review is conceived to briefly outline the important Bệnh viện Nội tiết Trung ƣơng historical milestones in surgery and intervention in patients with Fontan circulation, to describe the anatomic lesions and physiology of functional single ventricle, clinical approach to the management of patients with functional single ventricle, complications related to Fontan circulation and future perspectives

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