The results of total repair for tetralogy of fallot with an abnormal coronary artery

Anh Tien Do1,2, Ba Phong Nguyen1, Tran Thuy Nguyen1,2,
1 Trung tâm Tim mạch, Bệnh viện E
2 Trường ĐHYD, ĐHQGHN

Main Article Content

Abstract

The objective of this study evaluated the results of total repair for tetralogy of Fallot with an abnormal coronary artery.


Methods: This was a review of seri   Tetralogy of Fallot with an abnormal coronary artery cases who underwent total repair from 1/2018 to 6/2023.


Results: There were 10 patients who underwent complete surgical repair, include 6 males and 4 females. The mean age was 6,8 months  (range 4 months to 17 months)and the mean weight was 7,2 kilograms. 6 patients had Left Anterior Descending (LAD) artery originating from Right Coronary Artery (RCA), 3 patients with RCA originating from LAD and 1 patient with one major banche of RCA crossing the infundibulum. There were 7 patients with Pulmonary Valve Preserve (PVP) and 3 patients with Conduit Using (CU). The time of cardiopulmonary bypass, aortic clamping and ventilator were: 90 mins; 63 mins and 16 hours. There was not intrahospital mortality. Echocardiography post -operation: in PVP group all patient had a competence pulmonary valve and  mean gradient was 12,5 mmHg; in CU group, there were not pulmonary valve regurgitation and  mean gradient was 9 mmHg. During follow-up time 30 months after surgery, there was no late death; 2 patient in PVP group who had moderate pulmonary valve regurgitation and mean gradient was 22 mmHg; in CU group, there was a competence pulmonary valve with mean gradient 26 mmHg.


Conclusion: There was a good result of total repair for tetralogy of Fallot with an abnormal coronary artery.

Article Details

References

1. DiLorenzo M, Weinstein S, Shenoy R. Tetralogy of Fallot with Dextrocardia and Situs Inversus in a 7-Year-Old Boy. Tex Heart Inst J. 2013;40(4):481-483.
2. Husain AK, Khandeparkar JM, Tendolkar AG, Mulay AV. Surgical management of tetralogy of Fallot with anomalous coronary artery. J Postgrad Med. 1991;37(3):148-151.
3. Kalfa DM, Serraf AE, Ly M, Le Bret E, Roussin R, Belli E. Tetralogy of Fallot with an abnormal coronary artery: surgical options and prognostic factors. Eur J Cardio-Thorac Surg Off J Eur Assoc Cardio-Thorac Surg. 2012;42(3):e34-39. doi:10.1093/ejcts/ezs367
4. Kervancioglu M, Tokel K, Varan B, Yildirim SV. Frequency, origins and courses of anomalous coronary arteries in 607 Turkish children with tetralogy of Fallot. Cardiol J. 2011;18(5):546-551. doi:10.5603/cj.2011.0011
5. Kapur S, Aeron G, Vojta CN. Pictorial review of coronary anomalies in Tetralogy of Fallot. J Cardiovasc Comput Tomogr. 2015;9(6):593-596. doi:10.1016/j.jcct.2015.01.018
6. Koppel CJ, Jongbloed MRM, Kiès P, et al. Coronary anomalies in tetralogy of Fallot - A meta-analysis. Int J Cardiol. 2020;306:78-85. doi:10.1016/j.ijcard.2020.02.037
7. Dabizzi RP, Caprioli G, Aiazzi L, et al. Distribution and anomalies of coronary arteries in tetralogy of fallot. Circulation. 1980;61(1):95-102. doi:10.1161/01.cir.61.1.95
8. Park CS, Lee JR, Lim HG, Kim WH, Kim YJ. The long-term result of total repair for tetralogy of Fallot. Eur J Cardio-Thorac Surg Off J Eur Assoc Cardio-Thorac Surg. 2010;38(3):311-317. doi:10.1016/j.ejcts.2010.02.030