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Date Published: 24/10/2025
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DOI: 10.47972/vjcts.v53i.1547
Issue
Vol. 53
Section
Research Article
How to Cite
Nguyen, N. D., Nguyen, X. H., Nguyen, D. P., Dinh, T. D. D., Nguyen, D. D., & Bui, D. A. V. (2025). Surgical Repair of Anomalous Left Coronary Artery from the Pulmonary Artery in a Child: A Case Report from Hue Central Hospital and Literature Review. The Vietnam Journal of Cardiovascular and Thoracic Surgery, 53, 78 - 85. https://doi.org/10.47972/vjcts.v53i.1547

Surgical Repair of Anomalous Left Coronary Artery from the Pulmonary Artery in a Child: A Case Report from Hue Central Hospital and Literature Review

Nhu Dat Nguyen1, Xuan Hung Nguyen, Dang Phuoc Nguyen, Tran Duy Duy Dinh, Duc Dung Nguyen, Duc An Vinh Bui1,
1 Hue Central Hospital

Main Article Content

Abstract

Background: ALCAPA (Anomalous Left Coronary Artery from the Pulmonary Artery) is a rare congenital heart defect that, if left untreated, can lead to myocardial infarction, early heart failure, and death within the first year of life.


Methods: We present a clinical case of an infant diagnosed with ALCAPA and undergoing surgical restoration of the coronary system, together with a literature review.


Case report: A 3-month-old infant was initially admitted with a diagnosis of fulminant myocarditis and received intensive care. After hemodynamic improvement, echocardiography and computed tomography confirmed ALCAPA with moderate mitral regurgitation. The patient underwent direct reimplantation of the left coronary artery into the aorta. Postoperative recovery was favorable, with hospital discharge after 2 weeks. At 6-month follow-up, left ventricular ejection fraction was 66% and mitral regurgitation was mild.


Conclusion: ALCAPA carries a high risk of mortality and can easily be misdiagnosed as myocarditis, highlighting the need for early recognition and timely treatment. Surgery remains the standard of care, with direct reimplantation of the left coronary artery into the aorta being the preferred technique when anatomy is favorable.

Keywords

ALCAPA, coronary artery anomaly, coronary reimplantation, congenital heart surgery

Article Details

References

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