Case report: successful surgical treatment of supravalvular aortic stenosis

Truong Giang Le1, Trong Hai Hoang, Duy Hong Son Phung1,
1 Viet Duc University Hospital

Main Article Content

Abstract

Background: Supravalvular aortic stenosis (SVAS) is a rare congenital heart defect first described by Chevers in 1842. It accounts for approximately 8–14% of all congenital aortic stenosis cases and represents 0.05% of all congenital heart diseases. Surgical repair remains an effective primary treatment for this condition.


Case Presentation: This report describes a clinical case of SVAS successfully diagnosed and treated at Viet Duc University Hospital.


Results: A 27-year-old male patient was diagnosed with SVAS and underwent successful surgical reconstruction of the aortic root using the modified three-patch technique (Brom technique). Postoperative computed tomography (CT) scan at the 3-month follow-up showed favorable anatomical and hemodynamic outcomes.


Conclusion: Supravalvular aortic stenosis (SVAS) is a rare congenital condition associated with significant risks and potential complications. Aortic root reconstruction has proven to be an effective surgical approach, providing favorable long-term outcomes for patients.

Article Details

References

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