Case report; The first case of Uhl’anomaly in adult patient operated by Bidirectional Glenn Shunt at Cardiovascular Center of E Hospital

Nguyen Tran Thuy , Tran Dac Dai , Nguyen Cong Huu , Do Anh Tien , Le Tien Dung , Nguyen Do Hung , Nguyen Thai Long , Vu Xuan Quang , Le Ngoc Thanh

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Abstract

Uhl’s anomaly is characterized by complete or partial absence of the myocardium of the right ventricle, with ap-position of the endocardium and epicardium.We report a case of a 24-years-old female with Uhl’s anomaly who underwent successful Bidirectional Glenn Shunt in Cardiovascular of E Hospital Hanoi

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References

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