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Date Published: 29/01/2026
Abstract Views: 5
Views PDF: 5
DOI: 10.47972/vjcts.v54i.1626
Issue
Vol. 54
Section
Research Article
How to Cite
Le, T. K. V., & Le, Q. D. (2026). Pulmonary Artery Morphology on Computed Tomography and Cardiac Catheterization in Congenital Heart Disease Patients with Pulmonary Stenosis and Atresia at Cho Ray Hospital. The Vietnam Journal of Cardiovascular and Thoracic Surgery, 54, 24 - 32. https://doi.org/10.47972/vjcts.v54i.1626

Pulmonary Artery Morphology on Computed Tomography and Cardiac Catheterization in Congenital Heart Disease Patients with Pulmonary Stenosis and Atresia at Cho Ray Hospital

Thanh Khanh Van Le1,2, , Quoc Dat Le
1 Cho Ray Hospital
2 Tra Vinh College of Medicine and Pharmacy

Main Article Content

Abstract

Abstract: Pulmonary stenosis and pulmonary atresia are complex congenital heart defects with high variability in clinical presentation and pulmonary artery anatomy.


Research objective: To survey clinical and paraclinical characteristics, imaging characteristics of the pulmonary artery trunk and branches, and collateral circulation in patients with pulmonary artery stenosis and agenesis.


Methods: This retrospective descriptive study was conducted at the Pediatric Cardiac Surgery Intensive Care Unit, Cho Ray Hospital, from March 2017 to August 2023.


Results: Twenty-eight patients were evaluated, with a mean age of 5.13 ± 5.0 years. The most common symptoms were dyspnea (82%) and cyanosis (71%). On CT, pulmonary valve atresia was observed in 53.6% of cases, and 67.9% had no MAPCAs. Pulmonary artery confluence was present in 96.4% of cases. Among the 7 catheterizations performed, 57% revealed absence of the main pulmonary artery.


Conclusion: CT and cardiac catheterization are essential for comprehensive evaluation of pulmonary circulation anatomy in patients with pulmonary stenosis and atresia, providing critical information for treatment planning and improving surgical outcomes

Keywords

Pulmonary stenosis, pulmonary atresia, computed tomography, cardiac catheterization

Article Details

References

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