RESULTS OF SURGICAL REPAIR OF EBSTEIN’S ANOMALY AT HANOI HEART HOSPITAL

Nguyen Sinh Hien

Main Article Content

Abstract

Objectives: We sough to analyze the technical feature and results of surgical repair of Ebstein’s Anomaly with modified Carpentier’s technique in recovering function and anatomy of right ventricle and tricuspid valve to nearly normal state.
Methods: From August 2005 to December 2010, at Hanoi Heart Hospital we performed 52 surgical repairs of Ebstein’s Anomaly with modified Carpentier’s technique: Detachment of the posterior and septal leaflet and the adjacent part of the anterior leaflet to achieve extensive mobilization of the leaflet tissue; Vertical plication of the atrialized chamber and right atrium to reconstruct the right ventricle and
reduce the size of the dilated right atrium; Repositioning of the anterior and posterior leaflets at the tricuspid annulus to cover the entire orifice area with leaflet tissue at a normal level; Reinforcement of the tricuspid annulus with a prosthetic ring in cases with a very large orifice (Patients over 15 years); Closure of VSD, ASD, and mitral repair … for the associated cardiac anomalies.
Results: 52 patients with a mean age of 20 years (range 3 to 49 years) underwent repair. Comparative pre and postoperative data showed reduction tricuspid regurgitation grade from từ 3,72± 0,48 to 1,56± 0,48  (p < 0,01 ) and improvement in the functional class of heart failure (NYHA) from 2,53 ± 0,53 to 1,14± 0,35 (p < 0,01). No patients required reoperation. One early death (1,9%) occurred and was caused by sevre bleeding. The average follow- up is 42,42 months (range 17 to 81 months).
Conclusion: Whith modified Carpentier technique, our results of surgical repaire of Ebstein’s Anomaly in these 52 patients are satisfactory.

Article Details

References

1. Carpentier.A et al. A new reconstructive operation for Ebstein’s anomaly of the tricuspid valve. J Thorac Cardiovasc Surg 1988;96: 92-101
2. Carpentier.A . Malformations of the tricuspid valve and Ebstein’s anomaly. Surgery for congenital heart defects . W.B. Sauders company 2ed 1994: 615-622
3. Castaneda, Jonas, Mayer. Ebstein’s Anomaly. Cardiac Sugery of the Neonate and Infant. W. B.
Sauders company 1994: 273-280
4. Chen JM et al. Early and medium-term results for repair of Ebstein anomaly. The journal of Thoracic and Cardiovascular Surgey. 127, 4: 990-1000.
5. Chauvaud S et Carpentier A. Maladie d’Ebstein chirurgie conservatrice de la valve trcuspide et du ventricule droit selon les techniques actuelles. Encycl Med Chir (Elsevier, Paris ), Techniques chirugicales. Thorax, 42-841, 1999, 8p.
6. Chauvaud S, Berrebi A , Carpentier A. Ebstein’s anomaly: repair based on functional analysis. Euro Journal of Cardio-thoracic Surg 23 (2003) 525-31
7. Chauvaud S , Brancaccio G and Carpentier A. Cardiac Arrythmia in patients Undergoing Surgical Repair ò Ebstein’s Anomaly
8. Dearani JA , Danielson GK. Ebstein’s anomaly of the Tricuspid valve. Pediatric Cardiac
Surgery . Mosby 2003: 524-536.
9. Dupuis C. Maladie d’Ebstein, anomalie d’Uhl, Insuffisance tricuspide congenitale et anomalies voisines. Cardiologie pediatrique . Flammarion 1991: 389-398.
10. Kirklin, Barratt-Boyes. Ebstein Anomaly . Cardiac Surgery 3ed . Churchill Livingstone
2003: 1177-1199
11. Knott-Craig. Christopher J et al. Neonatal Repair of Ebstein’s Anomaly: Indications Surgical Technique, and Medium-Term Followup. Ann Thorac Surg 2000; 69:1505-10.
12. Hancock Friesen. Camille L et al. Posterior Annular Plication: Tricuspid Valve Repair in Ebstein’s Anomaly. Ann Thorac Surg 2004; 77: 2167-71.
13. Mohan Reddy.V et al. Repair of Congenital Tricuspid Valve Abnormalities With Artificial Chordae Tendineae. Ann Thorac Surg 1998; 66: 172-6
14. Marianeschi. SM et al. Alternative Approach to Repair of Ebstein’s Malformation: Intracardiac Repair With Ventricular Unloading. Ann Thorac Surg 1998; 66:1546-50.
15. Sarris GE , Giannopoulos NM et al. Results of surgery for Ebstein’s Anomaly: A multicenter stady from the European Congenital Heart Surgeons Association. J Thorac Cardiovasc
Surg 2006; 132: 50-57
16. Susan G. Maclellan- Tobert , Robert T. Feldt. Ebstein Anomaly of the tricuspid valve. Pediatric cardiovascular medecine. Churchill Livingstone 2000: 461-468.
17. Tanaka Masashi et al. Tricuspid Valve Supraannular Implantation in Adult Patients With Ebstein’s Anomaly. Ann Thorac Surg 2001;71:582-6
18. Ullmann. MV et al. Ventricularization of the Atrialized Chamber: A Concept of Ebstein’s Anomaly Repair. Ann Thorac Surg 2004;78:918-25.
19. Wu Qingyu et al. A New Procedure for Ebstein’s Anomaly. Ann Thorac Surg 2004;
77:470-6.
20. Nguyễn Sinh Hiền, Nguyễn Văn Mão và cộng sự. Kết quả bước đầu của phẫu thuật sửa chữa bệnh Ebstein tại Bệnh Viện Tim Hà Nội. Tạp chí Tim mạch học Việt Nam 2005; 42: 21- 29.
21. Nguyễn Sinh Hiền, Nguyễn Văn Mão và cộng sự. Kết quả ứng dụng phương pháp Carpentier trong phẫu thuật sửa chữa bệnh Ebstein tại Bệnh Viện Tim Hà Nội. Tạp chí Y học Việt nam 11-2006; 328:26-34.
22. Silva JP, Baumgratz JF, Fonseca L, Afiune JY, Franchi SM, Lopes LM, et al. Anomalia
de Ebstein: resultados com a reconstrução cônica da valva tricúspide. Arq Bras Cardiol. 2004;82(3):212-6.
23. Silva JP, Baumgratz JF, da Fonseca L, Franchi SM, Lopes LM, Tavares GM, et al. The cone reconstruction of the tricuspid valve in Ebstein's anomaly. The operation: early and midterm results. J Thorac Cardiovasc Surg. 2007;133(1):215-23.
24. Dearani J, Bacha E, da Silva JP. Cone reconstruction of the tricuspid valve for Ebstein's anomaly: anatomic repair. Oper Tech Thorac Cardiovasc Surg. 2008;13(1):109-25.